ADULT TYPE DERMATOMYOSITIDES
\ˈadʌlt tˈa͡ɪp dˈɜːmɐtˌɒmɪˌɒsɪtˌa͡ɪdz], \ˈadʌlt tˈaɪp dˈɜːmɐtˌɒmɪˌɒsɪtˌaɪdz], \ˈa_d_ʌ_l_t t_ˈaɪ_p d_ˈɜː_m_ɐ_t_ˌɒ_m_ɪ__ˌɒ_s_ɪ_t_ˌaɪ_d_z]\
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A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
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Word of the day
basidiomycota
- comprises fungi bearing the spores on basidium: Gasteromycetes (puffballs); Tiliomycetes (comprising orders Ustilaginales (smuts) and Uredinales (rusts)); Hymenomycetes (mushrooms; toadstools; agarics; bracket fungi); in some classification systems considered a division of kingdom comprises fungi bearing spores on a basidium; includes Gasteromycetes (puffballs) Tiliomycetes comprising the orders Ustilaginales (smuts) and Uredinales (rusts) Hymenomycetes (mushrooms, toadstools, agarics bracket fungi).